Abstract
Pheochromocytomas and paragangliomas (PPGLs) are neuroendocrine tumors derived from chromaffin cells of the adrenal medulla (pheochromocytomas) or from sympathetic/parasympathetic ganglia (paragangliomas). These tumors are one of the most inheritable forms of neoplasia, with 30-35% of PPGLs harboring germline pathogenic or likely pathogenic variants (PVs). In the Brazilian population, thi…